Combined orbital and ENT surgery successfully removed a large, rare orbital tumour located deep within the eye socket, while preserving vision for nine-year-old Stefan.

By the middle of last year, Jennifer Geoghegan noticed that her nine-year-old son Stefan had an increasingly protruding eye.

“It was eventually bulging prominently,” said Jennifer. “However, his vision wasn’t being affected, and there was no pain. So we eventually sought some medical advice.”

A biopsy revealed a solitary fibrous tumour – a benign, in Stefan’s case, and slow-growing tumour most commonly found in the lungs and very rare in paediatric populations. These lesions don’t respond well to chemotherapy or radiotherapy, which meant that surgical resection was Stefan’s next best option.

“The issue for surgical resection was the tumour’s location,” said Dr Krishna Tumuluri, ophthalmologist and oculoplastic surgeon who specialises in orbital disorders, and Stefan’s treating specialist.

“Because it extended back into the eye socket, where the orbit connects to the brain and houses the optic and a host of other nerves, a traditional approach entering via the eye socket would probably have put his vision at risk. It was also a large tumour, giving us very little space in which to manoeuvre.

“So we had to look at an endoscopic approach to give Stefan the best possible chance of removing the tumour while preserving his site.”

Dr Tumuluri talked to long-term colleague Macquarie University’s Professor Richard Harvey, who has trained with the world’s best rhinologists and skull base surgeons, and is unique in his ability to treat more serious and challenging orbital and sinus pathologies.

In October last year, they planned and performed a combined ENT–oculoplastic approach using the most advanced minimally invasive techniques for orbital and skull base tumours.

Through a 100 per cent endoscopic approach, the two surgeons used endonasal and transorbital approaches to reach the tumour and, in an 8-hour surgery, were able to remove the tumour. A small area of less than one per cent on the lateral aspect of the optic nerve remains for observation.

Dr Tumuluri and Professor Harvey used Macquarie University Hospital’s Theatre 12: a dedicated neurosurgery, orbital and skull base surgery space. It is equipped with the latest endoscopes, multi-image guidance systems and an intraoperative CT scanner – all highly advantageous for pinpoint accuracy in the brain area.
“Stefan’s recovery from the surgery was rapid,” said Jennifer. “The bulging, of course, was gone, with bruising and swelling much less than I would have expected. He was so well looked after by the Hospital’s brilliant nursing staff.

“Before the operation, Krishna had been lovely in talking to Stefan about the operation and what might happen afterwards, and we’d prepared him ourselves for possible partial or full loss of vision in his left eye – one of the biggest concerns.

“So there was that tense moment when the eye patch was removed after the procedure when Stefan woke up in Recovery. Was he going to have full vision or not?

“And then an elated: ‘He can see!’ from everyone. It was just phenomenal.”

Stefan returned home and is leading a normal life. He will undergo ongoing monitoring for the next five years.

“This is an excellent result for Stefan,” said Dr Tumuluri. “I didn’t imagine it would be such a great outcome. To have removed the tumour to such an extent without loss to vision is really a demonstration of the excellent patient outcomes that Macquarie University Hospital and others are increasingly able to bring to patients through such advanced surgical approaches using highly advanced imaging and other services.”